Maple Syrup Urine Disease (MSUD)- 1

Name: Maple Syrup Urine Disease (MSUD)- 1
Price: 975.00 INR
Availability: InStock

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IEM (Inborn errors of metabolism) Diets

Weight: 400 Gram

Description:

Metanutrition MSUD-1 is an amino acid based leucine, isoleucine and valine free powdered formula
Suitable for infants and children upto 3 years suffering from Maple Syrup Urine Disorder
Provides all other essential and non-essential amino acids, carbohydrates, fat, vitamins & minerals
Provides 15g protein / 100g of powder

Standard Dilution:

3 level scoop (25g) of MSUD-1 to be diluted in 100 ml of water

Precautions:

Use under medical supervision only
Not for parenteral use
Not suitable for use as a sole source of nutrition

₹975.00

SKU: N/A Category: IEM (Inborn errors of metabolism) Diets

Description

Nutrients	Per 100 g
Energy	493 Kcal
Protein	15 g
Carbohydrate	52 g
Fat	25 g

Amino acids
L-Histidine	500 mg
L-Isoluecine	–
L-Leucine	–
L-Lysine	1380 mg
L-Metheonine	475 mg
L-Cystine	350 mg
L-Phenylalanine	820 mg
L-Threonine	825 mg
L-Tryptophan	375 mg
L-Tyrosine	825 mg
L-Valine	–
L-Arginine	1100 mg
L-Alanine	1100 mg
L- Aspartic acid	1400 mg
L- Glutamic acid	2400 mg
Glycine	900 mg
L-Proline	1300 mg
L-Serine	900 mg
Glutamine	350 mg

Ingredients:

Maltodextrin, vegetable oils, corn starch, sugar, amino acids(L-Glutamic acid, L-Lysine Hydrochloride, L-Tyrosine, L-Proline, L-Arginine, L- Threonine, L-Serine, Glycine, L-Histidine, L-Methionine, L-Tryptophan, L-Cystine, L-Aspartic acid, L-Phenylalanine, L- Glutamine, L-Alanine), Tri calcium phosphate, Magnesium oxide, Ferric Pyrophosphate, Potassium Chloride, Zinc sulfate, Cupric sulphate, manganese sulfate, Potassium iodide, Sodium selenite, Sodium molybdate, Chromium picolinate, Choline chloride, Inositol, Ascorbic acid, Niacinamide, Calcium pantothenate, Pyridoxine hydrochloride, Thiamine chloride, Riboflavin, Vitamin D2, Folic acid, Biotin, Vitamin K1, Vitamin E Acetate, Vitamin A palmitate, Vitamin B12, Taurine, L- Carnitine.

Special indication:

For use in the dietary management of Maple Syrup Urine Disorder.

Leucine, Isoleucine and Valine free

Should be used under the supervision of doctor or physician

Administration guidelines:

The dosage is to be determined by your physician or dietitian. It depends on the age, weight and medical condition of the patient
This of not a sole source of nutrition
The diet should include natural protein, water and other nutrients in prescribed quantities. This is to supply the restricted amino acids to avoid further complications.
Foods high in carbohydrate and fat, but low in protein, should be provided to maintain or gain weight.

Direction for preparation and use:

Proper hygiene, handling and storage are important when preparing infant formula.
Use only the scoop provided. Each level scoop weighs 8g of Pristine Balance metanutrition powder.
When preparing any infant feed, please follow the guidelines below.
Wash hands thoroughly and clean the preparation area. Sterilize bottles and utensils using for preparation
Boil fresh water for 5 minutes and allow to cool.
Add prescribed amount of Pristine balance metanutrition powder and mix well.
Once the feed is prepared use the feed within one hour or discard unused food.