Methylmalonic Acidemia (MMA)-1/Propionic Acidemia-1, 400 g

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IEM (Inborn errors of metabolism) Diets

Description:

Metanutrition MMA/PA-1 is an amino acid based isoleucine, threonine, methionine & valine free powdered formula
Suitable for infants and children upto 3 years suffering from Methylmalonic Acidemia / Propionic Acidemia
Provides all other essential and non-essential amino acids, carbohydrates, fat, vitamins & minerals
Provides 15g protein / 100g of powder

Standard Dilution:

3 level scoop (25g) of MMA/PA-1 to be diluted in 100 ml of water

Precautions:

Use under medical supervision only
Not for parenteral use
Not suitable for use as a sole source of nutrition

₹1,540.00

SKU: N/A Category: IEM (Inborn errors of metabolism) Diets

Description

Nutrients	Per 100 g
Energy	493 Kcal
Protein	15 g
Carbohydrate	52 g
Fat	25 g
DHA mg	25 mg
Linoleic Acid	3000 mg

Amino acids
L-Histidine	475 mg
L-Isoleucine	–
L-Leucine	2400 mg
L-Lysine	1500 mg
L-Methionine	–
L-Cystine	300 mg
L-Phenylalanine	625 mg
L-Threonine	–
L-Tryptophan	350 mg
L-Tyrosine	725 mg
L-Valine	–
L-Arginine	975 mg
L-Alanine	3400 mg
L- Aspartic acid	1275 mg
L- Glutamic acid	–
Glycine	975 mg
L-Proline	1275 mg
L-Serine	725 mg
Glutamine	–

Ingredients:

Maltodextrin, Vegetable Oils, Corn Starch, Sugar, Fructose, Amino Acids(L-Glutamic acid, L-Leucin, L-Lysin, Hydrochloride, L-Tyrosine, L-Proline, L-Valin, L-Isoleucine, L-Alanine, L-arginine, L-Threonine, L-Threonine, L-Serinr, Glycine, L-Histidine, L-Metheonine, L-Tryptophan, L-Cystine, L-Aspertic acis), Tri Calcium Phosphate, Magnesium Oxide, Ferric Pyrophosphate, Pottasium Cholride, Zinc sulfate, Cupric Sulphate, Manganese Sulfate,Potasium iodide, Sodim Selenite, Sodium Molybdate, Chromium Picolinate, Choline Chloride, Inositil, Ascorbic Acid, Niacinamide, Calcium pantothenate, Pyridoxine Hydrochloride, Thiamin,hydrochloride, Riboflavin, Vitamin D2, Folic Acid, Biotin, Vitamin K1, Vitamin E Acetate, Vitamin A palmitate, Vitamin B12, Taurine, L- Carnintine, DHA.

Special indication:

For use in the dietary management of Methylmalonic Acidemia/Propionic Acidemia.

Isoleucine, Methionine Threonine and Valine free

Should be used under the supervision of doctor or physician.

Administration guidelines:

The dosage is to be determined by your physician or dietitian. It depends on the age, weight and medical condition of the patient
This of not a sole source of nutrition
The diet should include natural protein, water and other nutrients in prescribed quantities. This is to supply the restricted amino acids to avoid further complications.
Foods high in carbohydrate and fat, but low in protein, should be provided to maintain or gain weight.

Direction for preparation and use:

Proper hygiene, handling and storage are important when preparing infant formula.
Use only the scoop provided. Each level scoop weighs 8g of Pristine Balance metanutrition powder.
When preparing any infant feed, please follow the guidelines below.
Wash hands thoroughly and clean the preparation area. Sterilize bottles and utensils using for preparation
Boil fresh water for 5 minutes and allow to cool.
Add prescribed amount of Pristine balance metanutrition powder and mix well.
Once the feed is prepared use the feed within one hour or discard unused food.