Metanutrition Methylmalonic Acidemia / Propionic Acidemia-1 (MMA/PA-1) 400g

Ingredients:
Maltodextrin, Vegetable Oils, Corn Starch, Sugar, Fructose, Amino Acids(L-Glutamic acid, L-Leucin, L-Lysin, Hydrochloride, L-Tyrosine, L-Proline, L-Valin, L-Isoleucine, L-Alanine, L-arginine, L-Threonine, L-Threonine, L-Serinr, Glycine, L-Histidine, L-Metheonine, L-Tryptophan, L-Cystine, L-Aspertic acis), Tri Calcium Phosphate, Magnesium Oxide, Ferric Pyrophosphate, Pottasium Cholride, Zinc sulfate, Cupric Sulphate, Manganese Sulfate,Potasium iodide, Sodim Selenite, Sodium Molybdate, Chromium Picolinate, Choline Chloride, Inositil, Ascorbic Acid, Niacinamide, Calcium pantothenate, Pyridoxine Hydrochloride, Thiamin,hydrochloride, Riboflavin, Vitamin D2, Folic Acid, Biotin, Vitamin K1, Vitamin E Acetate, Vitamin A palmitate, Vitamin B12, Taurine, L- Carnintine, DHA.

Shelf Life: Best before 12 months from date of manufacture

Instructions for Preparation/ Use:
Proper hygiene, handling and storage are important when preparing formula.
Use only the scoop provided.
Each level scoop weighs 8g of Pristine Balance Metanutrition powder.

Standard Dilution:
3 level scoop (25g) of MMA/PA-1 to be diluted in 100 ml of water; Serve Size: 25g

When preparing any feed, please follow the guidelines below:
First wash hands thoroughly and clean the preparation area. Sterilize bottles and utensils using for preparation
Boil fresh water for 5 minutes and allow to cool.
Add prescribed amount of Pristine Balance Metanutrition MMA/PA-1 powder and mix well.
Once the feed is prepared use the feed within one hour or discard unused food.

Storage: Store in cool and dry place away from strong odour and sunlight.

Age: For infants and children upto 3 years of age

Safety Precautions:
Use under medical supervision only
Not for intravenous/ parenteral use
Not to be used by pregnant, nursing and lactating women, or by infants and children , except when medically advised.
Not a sole source of nutrition

Administration Guidelines:
Isoleucine, threonine, methionine and valine free supplement- should be used under the supervision of doctor or physician.
The dosage is to be determined by your physician or dietitian. It depends on the age, weight and medical condition of the patient
The diet should include natural protein, water and other nutrients in prescribed quantities. This is to supply the restricted amino acids to avoid further complications.
Foods high in carbohydrate and fat, but low in protein, should be provided to maintain or gain weight.

Nutrients	Per 100 g
Energy	483 Kcal
Protein	15 g
Protein Equivalent	12.5 g
Carbohydrate	52 g
Fat	25 g
DHA	25 mg
Linoleic Acid	3000 mg
AMINO ACIDS
L-Histidine	475 mg
L-Isoleucine	–
L-Leucine	2400 mg
L-Lysine	1500 mg
L-Methionine	–
L-Cystine	300 mg
L-Phenylalanine	625 mg
L-Threonine	–
L-Tryptophan	350 mg
L-Tyrosine	725 mg
L-Valine	–
L-Arginine	975 mg
L-Alanine	3400 mg
L-Aspartic acid	1275 mg
L-Glutamic acid	–
Glycine	975 mg
L-Proline	1275 mg
L-Serine	725 mg
Glutamine	–

balance metanutrition, IEM, inborn errors of metabolism diets, Methylmalonic acidemia/ Propionic acidemia, MMA/PA-1, nutritional supplement, nutritional care